Adult-Onset Congenital Cystic Adenomatoid Malformation in Combination with Intralobar Bronchopulmonary Sequestration: a case report
نویسندگان
چکیده
Congenital cystic adenomatoid malformation (CCAM) and bronchopulmonary sequestration are congenital lung lesions. They are classified as separate entities. Each of them has distinct embryology, pathology, and natural history. However there are some commonalities between them. CCAM may have a pulmonary artery supply, or be supplied like a sequestration from the aorta, and histological features of both lesions may coexist [1]. CCAM is usually diagnosed before the age of 2. It is rarely encountered in adult [2]. We present an adult case of congenital cystic adenomatoid malformation in combination with intralobar bronchopulmonary sequestration.
منابع مشابه
Intralobar bronchopulmonary sequestration: antenatal diagnosis.
A child with the antenatal diagnosis of pulmonary cystic adenomatoid malformation underwent thoracotomy and an intralobar bronchopulmonary sequestration was found. Histological examination of the resected specimen showed cystic adenomatoid malformation within the sequestered segment.
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BACKGROUND Sequestration with associated cystic adenomatoid malformation is rare. A study was undertaken to determine whether pulmonary sequestration associated with congenital cystic adenomatoid malformation has a more favourable natural history than that of sequestration without associated cystic adenomatoid malformation. METHODS An outline of the postnatal work up leading to the management...
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Congenital lung lesions that can be diagnosed on the basis of prenatal sonography include cystic adenomatoid malformations and extrapulmonary bronchopulmonary sequestrations. Intralobar bronchopulmonary sequestration is a rare congenital malformation of the lung. The prenatal sonographic features of this condition are reported here.
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